Hereditary Hemorrhagic Telangiectasia

Kuehnel, Thomas and Wirsching, Kornelia and Wohlgemuth, Walter and Chavan, Ajay and Evert, Katja and Vielsmeier, Veronika (2018) Hereditary Hemorrhagic Telangiectasia. OTOLARYNGOLOGIC CLINICS OF NORTH AMERICA, 51 (1). 237-+. ISSN 0030-6665, 1557-8259

Full text not available from this repository. (Request a copy)

Abstract

Hereditary hemorrhagic telangiectasia (HHT) describes the presenting manifestations of a disorder that is characterized by pathologic blood vessels. HHT is inherited as an autosomal dominant trait with variable penetrance. The abnormal vascular structures (dysplasias) can affect all the organs in the human body. The link between a physical stimulus and new lesion development has been established for mucosal trauma owing to nasal airflow turbulence, for ultraviolet exposure to the fingers, and for mechanical trauma to the dominant hand. The pressing question then is whether HHT treatment constitutes a stimulus that is sufficient to trigger new lesion development.

Item Type: Article
Uncontrolled Keywords: PULMONARY ARTERIOVENOUS-MALFORMATIONS; WEBER-RENDU-SYNDROME; QUALITY-OF-LIFE; HEPATIC VASCULAR MALFORMATIONS; SEPTAL DERMOPLASTY; ANGIOGRAPHIC EMBOLIZATION; ENDOVASCULAR TREATMENT; ARTERY EMBOLIZATION; JUVENILE POLYPOSIS; CONTROLLED-TRIAL; Hereditary hemorrhagic telangiectasia; Dysplasias; Osler-Weber-Rendu syndrome; Mucocutaneous lesions
Subjects: 600 Technology > 610 Medical sciences Medicine
Divisions: Medicine > Lehrstuhl für Hals-Nasen-Ohren-Heilkunde
Medicine > Lehrstuhl für Pathologie
Depositing User: Dr. Gernot Deinzer
Date Deposited: 20 Mar 2020 14:25
Last Modified: 20 Mar 2020 14:25
URI: https://pred.uni-regensburg.de/id/eprint/15164

Actions (login required)

View Item View Item