Juergens, T. P. and Schulte-Mattler, W. J. (2006) Myotonic syndromes and differential diagnosis of myotonic discharges in the EMG. KLINISCHE NEUROPHYSIOLOGIE, 37 (2). pp. 151-160. ISSN 1434-0275,
Full text not available from this repository. (Request a copy)Abstract
Myotonic discharges in concentric needle electromyography are often considered to be diagnostic for myotonic disorders. However, electromyographic spontaneous activity that can be mistaken for myotonic discharges may occur in a variety of other disorders, such as neuromyotonia, Schwartz-jampel syndrome, myosites, glycogenoses, a few rare myopathies, and in chronic neurogenic disorders. Myotonic discharges are always present in chloride channel myotonias and frequently in patients with one of the myotonic dystrophies. Myotonic discharges are a frequent finding in patients with sodium channelopathy, but in some patients they occur only by provoking their occurrence via local muscle cooling, work, or potassium load. So far, myotonic discharges have never occurred in patients with periodic paralyses not caused by altered sodium channels. Based on this fact we present pointers to differential diagnosis of myotonic dystrophies and muscle channelopathies as well as to differential diagnosis of myotonic discharges and similar EMG findings.
| Item Type: | Article |
|---|---|
| Uncontrolled Keywords: | HYPOKALEMIC PERIODIC PARALYSIS; MUSCLE SODIUM-CHANNEL; SKELETAL-MUSCLE; ANDERSENS-SYNDROME; DYSTROPHY TYPE-2; MUTATIONS; CONGENITA; CHANNELOPATHIES; INACTIVATION; FLUCTUANS; electromyography; myotonia; myotonic discharges; spontaneous activity; channelopathy |
| Subjects: | 600 Technology > 610 Medical sciences Medicine |
| Divisions: | Medicine > Lehrstuhl für Neurologie |
| Depositing User: | Dr. Gernot Deinzer |
| Date Deposited: | 15 Feb 2021 07:09 |
| Last Modified: | 15 Feb 2021 07:09 |
| URI: | https://pred.uni-regensburg.de/id/eprint/34513 |
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