Koegel, Julian and Berneburg, Mark and Karrer, Sigrid and Drexler, Konstantin and Niebel, Dennis (2023) Multilocular pyoderma gangrenosum Association with primary manifestation of primary biliary cholangitis. DERMATOLOGIE, 74. pp. 538-542. ISSN 2731-7005, 2731-7013
Full text not available from this repository. (Request a copy)Abstract
A 16-year-old female patient with previously diagnosed acne vulgaris was transferred to our clinic in reduced general condition with rapidly progressive and extremely painful ulcerations. In the laboratory exam, inflammatory parameters were highly elevated, but she was normothermic. Based on the findings, we diagnosed multilocular pyoderma gangrenosum. Further investigations established the diagnosis of primary biliary cholangitis as the underlying condition. Treatment with systemic corticosteroids was initiated and we started therapy with ursodeoxycholic acid. This led to improvement within a few days. PAPA-syndrome (pyogenic arthritis, pyoderma gangrenosum and acne vulgaris) could be ruled out by genetic analysis.
| Item Type: | Article |
|---|---|
| Uncontrolled Keywords: | Sweet's syndrome; Neutrophilic dermatosis; Primary biliary cholangitis; PAPA syndrome; Ulceration |
| Subjects: | 600 Technology > 610 Medical sciences Medicine |
| Divisions: | Medicine > Lehrstuhl für Dermatologie und Venerologie |
| Depositing User: | Dr. Gernot Deinzer |
| Date Deposited: | 05 Mar 2024 07:52 |
| Last Modified: | 05 Mar 2024 07:52 |
| URI: | https://pred.uni-regensburg.de/id/eprint/59260 |
Actions (login required)
 |
View Item |
